Revue de Pneumologie Clinique – Vol. 69 – N° 1 – p. – La maladie de Castleman: observations inhabituelles et revue de la littérature – EM|consulte. Disease definition. Castleman disease (CD) is a benign lymphoproliferative disorder that may present as a localized or multicentric form (see these terms). Introduction La maladie de Castleman (MC) est une affection rare, caractérisée par l’existence d’une forme localisée et d’une forme.

Author: Shakazragore Tygokora
Country: Nicaragua
Language: English (Spanish)
Genre: Literature
Published (Last): 23 May 2013
Pages: 398
PDF File Size: 8.94 Mb
ePub File Size: 15.88 Mb
ISBN: 707-3-57051-115-9
Downloads: 94274
Price: Free* [*Free Regsitration Required]
Uploader: Toshakar

Access to the full text of this article requires a subscription. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted.

Exacerbations castlemab clinical symptoms in human casyleman virus type 1-infected patients with multicentric Castleman’s disease are associated with a high increase in Kaposi’s sarcoma herpesvirus DNA load in peripheral blood mononuclear cells. Identification of two homologs of the Kaposi’s sarcoma-associated herpesvirus human herpesvirus 8 in retroperitoneal fibromatosis of different macaque species.

There was a problem providing the content you requested

Dysregulated interleukin 6 expression produces a syndrome resembling Castleman’s disease in mice. Interleukin-6 gene expression in Castleman’s disease.


Molecular mimicry of human cytokine and cytokine response pathway genes by KSHV. The third one is a plasma cell form with monoclonal proliferation associated with a monoclonal gammapathy.

They underlie the difficulty of surgical resection due to the tumor vascularization. Angiofollicular ganglionic hyperplasia Angiofollicular lymph hyperplasia Prevalence: If you are a subscriber, please sign in ‘My Account’ at the top right of the screen.

Br J Haematol These three cases highlight the polymorphic clinical and radiological features of Castleman disease. Other search option s Alphabetical list. The pathological features and the therapeutic management of CD are discussed. J Exp Med Malladie and hematopoiesis induced by Kaposi’s sarcoma-associated herpesvirus-encoded interleukin As per the Law relating to information storage and personal integrity, you have the right to oppose art 26 of that lawaccess art 34 of that law and rectify art 36 of that law your personal data.

Journal page Archives Contents list. Journal page Archives Contents list. Human herpesvirus type 8 interleukin-6 homologue is functionally active on human myeloma cells. Nous rapportons trois observations de maladie de Castleman unicentrique. Two forms have been described: Cas cliniques Observation 1. Preoperative diagnosis can be difficult with a thymoma or a lymphoma.

Cellular tropism and viral interleukin-6 expression distinguish human herpesvirus 8 involvement in Kaposi’s sarcoma, primary effusion lymphoma, and multicentric Castleman’s disease.


An unusual cluster of cases of Castleman’s disease during highly active antiretroviral therapy for AIDS. Scherpereel abcM. Human herpesvirus 8 encodes a homolog of interleukin Only comments written in English can be processed.

Accueil du site de la malade de CASTLEMAN

Tacelli fJ. Detailed information Professionals Summary information Greekpdf. Access to the full text of this article requires a subscription.

Because of the risk of relapse and malignant transformation, long-term follow-up is mandatory. A report of two cases and a review of the literature. N Engl J Med Top of the page – Article Outline. The owners of this website hereby guarantee to respect the legal confidentiality conditions, applicable in France, and not to disclose this data to third parties.

We report three cases of monocentric Castleman disease.

Contact Help Who are we? Additional information Further information on this disease Classification s 2 Gene s 0 Other website s 6. Remy-Jardin bfA. Specialised Social Services Eurordis directory.